Scimitar syndrome in infancy

Pulmonary hypertension in scimitar syndrome in infancy.

Four infants with the scimitar syndrome presented with failure to thrive, cardiac failure, and pulmonary hypertension. In all cases systemic arteries arose from the upper abdominal aorta to perfuse the lower part of the right lung, and a large unobstructed anomalous pulmonary vein drained venous blood from almost the entire right lung to the inferior vena cava. An additional small pulmonary vei...

[Scimitar syndrome].

80 Background --Scimitar syndrome, which presents with an anomalous right pulmonary vein that drains part or the entire right lung into the inferior vena cava (IVC) as its hallmark, is a rare association of congenital cardiopulmonary anomalies with an incidence of approximately 1 to 3 per 100,000 live births worldwide. It commonly presents with symptoms of respiratory distress and has an over-a...

Scimitar syndrome.

Scimitar syndrome is a relatively uncommon constellation of cardio-pulmonary anomalies, its typical feature being partial anomalous pulmonary venous connection. It can present in the neonatal period as well as later in life. We present the case of a girl diagnosed in the newborn period, along with a brief review of literature.

Scimitar syndrome in infancy. Role of embolisation of systemic arterial supply to right lung.

Re-Sheathing the Scimitar Syndrome

Scimitar Syndrome is a congenital condition resulting in anomalous pulmonary venous drainage from the lung into the inferior vena cava. It is often associated with cardiac and pulmonary abnormalities, both which are determinants in the severity and timing of presentation. True incidence of this condition is unknown and likely to be significantly underestimated as many patients remain asymptomat...